Right ventricular outflow tract obstruction pulmonary subvalvular stenosis

Associate Editor-In-Chief:

Associate Editor-in-Chief: Keri Shafer, M.D. [mailto:kshafer@bidmc.harvard.edu]

Anatomy

 * There is hypertrophy of the infundibular muscle causing obstruction.


 * The isolated form is rare, more commonly develops in response to an underlying VSD.

Clinical Features

 * Similar to valvar pulmonic stenosis.


 * No ejection click in contrast to valvar pulmonic stenosis.


 * No poststenotic dilation of the pulmonary artery in contrast to valvar pulmonic stenosis.