Right ventricular outflow tract obstruction pathophysiology

Pathophysiology
The right ventricular outflow tract obstruction includes stenosis or narrowing of the pulmonary valve, the tissue above the valve (supravalvar obstruction) and below it(subvalvar obstruction). Congenital subvalvar and supravalvar right ventricular outflow tract stenosis usually occurs with other congenital heart defects such as Ventricular Septal Defect (VSD) or Tetralogy of Fallot.

If right ventricular outflow tract obstruction is present and the ventricular septum is intact, usually the right ventricle will adapt better given that no right to left shunting is present. This absence of shunting may result in sufficient pulmonary blood flow to allow the patient to remain asymptomatic longer.