Corneal dystrophy

Human corneal dystrophies is a group of disorders, characterised by a noninflammatory, inherited, bilateral opacity of the transparent front part of the human eye called the cornea. There is a number of rare forms varying in expression and degree of vision loss.

The International Committee for Classification of Corneal Dystrophies (IC3D) was established in 2005 and created a new classification system employing the latest data of molecular biology an genetics.

List

 * Fuchs' dystrophy
 * Macular corneal dystrophy
 * Reis-Bucklers corneal dystrophy (CDB1)
 * Thiel-Behnke dystrophy (CDB2)
 * Meesmann juvenile epithelial corneal dystrophy (MECD, Stocker-Holt dystrophy, OMIM 122100)
 * Gelatinous drop-like corneal dystrophy
 * Subepithelial mucinous corneal dystrophy
 * Lisch epithelial dystrophy
 * Granular corneal dystrophy type I
 * Granular corneal dystrophy type II (also Avellino corneal dystrophy)
 * Lattice corneal dystrophy type I
 * Lattice corneal dystrophy type II
 * Fleck dystrophy
 * Schnyder corneal dystrophy
 * Posterior amorphous corneal dystrophy
 * Congenital stromal dystrophy (CSCD)
 * Posterior polymorphous dystrophy type 1
 * Posterior polymorphous dystrophy type 2
 * Posterior polymorphous dystrophy type 3
 * Congenital endothelial dystrophy type 1 (CHED1)
 * Congenital endothelial dystrophy type 2 (CHED2)
 * X-linked endothelial corneal dystrophy
 * Epithelial basement membrane dystrophy (OMIM 121820), called a corneal dystrophy but in reality this condition is not inherited in the majority of cases, representing a non-specific reaction to a variety of corneal insults.

Other conditions affecting cornea

 * Keratoconus
 * Keratoglobus