Right ventricular outflow tract obstruction pulmonary supravalvular stenosis

Associate Editor-In-Chief:

Associate Editor-in-Chief: Keri Shafer, M.D. [mailto:kshafer@bidmc.harvard.edu]

Anatomy
1. Also called peripheral pulmonary stenosis.

2. May have one or many stenoses of the PA or its branches.

3. Infrequently occurs as an isolated lesion, more commonly occurs as part of Tetralogy of Fallot.

Clinical Features
1. The murmur is most prominent at the upper left sternal border, axillae, and the posterior lung fields.