Total anomalous pulmonary venous connection surgery

Associate Editor-In-Chief:; Keri Shafer, M.D. [mailto:kshafer@bidmc.harvard.edu] Priyamvada Singh, MBBS mailto:psingh@perfuse.org

Assistant Editor-In-Chief: Kristin Feeney, B.S. mailto:kfeeney@perfuse.org

Overview
Due to the poor prognosis in untreated patients, surgery should be performed as soon as possible.

Surgical Therapy


Surgery should be performed as soon as possible in the patients of total anomalous pulmonary venous connection. The surgical procedure varies depending upon the anatomy of the TAPVC lesion.


 * Supracardiac and Infracardiac TAPVC- Connection is created between the pulmonary veins and the left atrium. The vertical vein is tied up so that the abnormal blood flow could be prevented.
 * Pulmonary veins directly connected to the superiorvenacava - An intracardiac baffle is created that helps in transfer of blood from the right atrium, through atrial septum into the left atrium.
 * Intracardiac (pulmonary vein connected to the coronary sinus)- Coronary sinus is incised and connected to left atrium.
 * Intracardiac (pulmonary vein opening directly into the right atrium)- A interatrial connection is made and the blood is redirected from right atrium to left atrium