Bernard-Soulier syndrome

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Bernard-Soulier syndrome Classification and external resources
ICD-10	D69.1
ICD-9	287.1
OMIM	231200
DiseasesDB	1356
eMedicine	ped/230
MeSH	D001606

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Guidelines / Policies / Govt
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Bernard-Soulier syndrome (BSS, named after Jean Bernard and Jean Pierre Soulier) is a medical condition. this condition is a disorder of the vWF(vonWillebrand factor) receptor termed glycoprotein Ib(GpIb). It presents as a bleeding disorder due to the inability of platelets to bind and aggregate at sites of vascular endothelial injury.

External links

• BSS site

See also

• Gray platelet syndrome
• Glanzmann's thrombasthenia
• von Willebrand disease
• May-Hegglin anomaly

v • d • e Pathology: hematology (primarily D50-D77, 280-289)
RBCs/anemia/ hemoglobinopathy (Myeloid)	nutritional anemia: Iron deficiency anemia, Plummer-Vinson syndrome, Megaloblastic anemia (Pernicious anemia) hereditary hemolytic anemia: enzyme disorders (G6PD Deficiency, Pyruvate kinase deficiency,Triosephosphate isomerase deficiency), Thalassemia, Sickle-cell disease/trait, Hereditary spherocytosis, Hereditary elliptocytosis, Hereditary stomatocytosis acquired hemolytic anemia: Autoimmune (Warm), HUS, MAHA, PNH, PCH aplastic anemia: Acquired PRCA, Diamond-Blackfan anemia, Fanconi anemia • Sideroblastic anemia
Coagulation/platelets (Myeloid)	coagulopathy: DIC (Congenital afibrinogenemia, Purpura fulminans) • Hemophilia (A/VII, B/IX, C/XI, XIII) • Von Willebrand disease Purpura: Henoch-Schönlein, ITP (Evans syndrome), TTP primary hypercoagulable state: Protein C deficiency - Protein S deficiency - Antithrombin III deficiency - Factor V Leiden - Activated protein C resistance - Antiphospholipid syndrome other hemorrhagic conditions: Bernard-Soulier syndrome - Glanzmann's thrombasthenia - Grey platelet syndrome - May Hegglin anomaly Essential thrombocytosis - Thrombocytopenia
Monocytes/Macrophages (Myeloid)	WHO-I histiocytosis (Langerhans cell histiocytosis) WHO-II/non-Langerhans-cell histiocytosis (Juvenile xanthogranuloma, Hemophagocytic lymphohistiocytosis) WHO-III/malignant histiocytic disorders (Acute monocytic leukemia, Malignant histiocytosis, Erdheim-Chester disease) -cytosis: Monocytosis -penia: Monocytopenia
Granulocytes (Myeloid)	-cytosis: granulocytosis (Neutrophilia, Eosinophilia, Basophilia) -penia: Granulocytopenia/agranulocytosis (Neutropenia, Kostmann syndrome)
Other/general myeloid	Chronic granulomatous disease
Lymphoid	-cytosis: Lymphocytosis -penia: Lymphopenia
Other	Asplenia/hyposplenism - Methemoglobinemia - Pancytopenia
See also hematological malignancy and immune disorders

v • d • e WikiDoc Research Resources for Bernard-Soulier syndrome (Click show to right to view)
Articles on Bernard-Soulier syndrome	Most recent articles on Bernard-Soulier syndrome • Most cited articles on Bernard-Soulier syndrome • Review articles on Bernard-Soulier syndrome • Articles on Bernard-Soulier syndrome in N Eng J Med, Lancet, BMJ
Media (Slides, Video, Images, MP3) on Bernard-Soulier syndrome	Powerpoint slides on Bernard-Soulier syndrome • Images of Bernard-Soulier syndrome • Photos of Bernard-Soulier syndrome • Podcasts & MP3s on Bernard-Soulier syndrome • Videos on Bernard-Soulier syndrome
Evidence Based Medicine Regarding Bernard-Soulier syndrome	Cochrane Collaboration on Bernard-Soulier syndrome • Bandolier on Bernard-Soulier syndrome • TRIP on Bernard-Soulier syndrome
Cost Effectiveness of Bernard-Soulier syndrome	Cost Effectiveness of Bernard-Soulier syndrome
Clinical Trials Involving Bernard-Soulier syndrome	Ongoing Trials on Bernard-Soulier syndrome at Clinical Trials.gov • Trial results on Bernard-Soulier syndrome • Clinical Trials on Bernard-Soulier syndrome at Google
Guidelines / Policies / Government Resources (FDA/CDC) Regarding Bernard-Soulier syndrome	US National Guidelines Clearinghouse on Bernard-Soulier syndrome • NICE Guidance on Bernard-Soulier syndrome • NHS PRODIGY Guidance • FDA on Bernard-Soulier syndrome • CDC on Bernard-Soulier syndrome
Textbook Information on Bernard-Soulier syndrome	Books and Textbook Information on Bernard-Soulier syndrome
Pharmacology Resources on Bernard-Soulier syndrome	Dosing of Bernard-Soulier syndrome • Drug interactions with Bernard-Soulier syndrome • Side effects of Bernard-Soulier syndrome • Allergic reactions to Bernard-Soulier syndrome • Overdose information on Bernard-Soulier syndrome • Carcinogenicity information on Bernard-Soulier syndrome • Bernard-Soulier syndrome in pregnancy • Pharmacokinetics of Bernard-Soulier syndrome •
Genetics, Pharmacogenomics, and Proteinomics of Bernard-Soulier syndrome	Genetics of Bernard-Soulier syndrome • Pharmacogenomics of Bernard-Soulier syndrome • Proteomics of Bernard-Soulier syndrome
Newstories on Bernard-Soulier syndrome	Bernard-Soulier syndrome in the news • Be alerted to news on Bernard-Soulier syndrome • News trends on Bernard-Soulier syndrome
Commentary on Bernard-Soulier syndrome	Blogs on Bernard-Soulier syndrome
Patient Resources on Bernard-Soulier syndrome	Patient resources on Bernard-Soulier syndrome • Discussion groups on Bernard-Soulier syndrome • Patient Handouts on Bernard-Soulier syndrome • Directions to Hospitals Treating Bernard-Soulier syndrome • Risk calculators and risk factors for Bernard-Soulier syndrome
Healthcare Provider Resources on Bernard-Soulier syndrome	Symptoms of Bernard-Soulier syndrome • Causes & Risk Factors for Bernard-Soulier syndrome • Diagnostic studies for Bernard-Soulier syndrome • Treatment of Bernard-Soulier syndrome
Continuing Medical Education (CME) Programs on Bernard-Soulier syndrome	CME Programs on Bernard-Soulier syndrome
International Resources on Bernard-Soulier syndrome	Bernard-Soulier syndrome en Espanol • Bernard-Soulier syndrome en Francais
Business Resources on Bernard-Soulier syndrome	Bernard-Soulier syndrome in the Marketplace • Patents on Bernard-Soulier syndrome
Informatics Resources on Bernard-Soulier syndrome	List of terms related to Bernard-Soulier syndrome

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Acknowledgement and Attribution Regarding Sources of Content

Some of the initial content on this page may be incorporated in part from copyleft sources in the public domain including wikis such as Wikipedia and AskDrWiki. Drug information for patients came from the The National Library of Medicine. Infectious disease information may have come from the Centers for Disease Control (CDC). Differential Diagnoses are drawn from clinicians as well as an amalgamation of 3 sources: 1.The Disease Database; 2. Kahan, Scott, Smith, Ellen G. In A Page: Signs and Symptoms. Malden, Massachusetts: Blackwell Publishing, 2004:3; 3. Sailer, Christian, Wasner, Susanne. Differential Diagnosis Pocket. Hermosa Beach, CA: Borm Bruckmeir Publishing LLC, 2002:7 .