Pityriasis rubra pilaris
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| Pityriasis rubra pilaris Classification and external resources | |
 | |
|---|---|
| ICD-10 | L44.0 |
| ICD-9 | 696.4 |
| OMIM | 173200 |
| DiseasesDB | 29305 |
| MedlinePlus | 001471 |
| eMedicine | derm/337 |
| MeSH | D010916 |
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Pityriasis rubra pilaris (PRP) is a rare and chronic skin disorder that often has a sudden onset. Symptoms may include reddish-orange patches (Latin: rubra) on the skin, severe flaking (Latin: pityriasis), uncomfortable itching, thickening of the skin on the feet and hands, and thickened bumps around hair follicles (Latin: pilus for hair). For some, early symptoms may also include generalized swelling of the legs, feet and other parts of the body. PRP has a varied clinical progression and a varied rate of improvement. There is no known cause or cure.
It was first described by Marie-Guillaume-Alphonse Devergie in 1856,[1] and the condition is also known as Devergie's disease.[2]
Classification
Dr. W.A.D. Griffiths, from Great Britain, classified six forms of PRP in the early 1980s.[3] At this time, the causes of PRP are still unknown and symptoms can be difficult to diagnose. Frequently, more than one medical professional will be consulted before an accurate PRP diagnosis is made.
Dermatologists have identified both an acquired form and an inherited form (familial) of PRP and have described them in medical journals. The acquired form usually shows a spontaneous or gradual remission of symptoms within several years although long-term symptoms may continue for years. The inherited form starts early in childhood with persistent long-term symptoms into adulthood.
Although most people who develop PRP are over age 50, individuals of any age, race, and nationality can be affected. Women and men seem to be equally affected.
References
- ↑ Devergie M. G. A. (1856). "[Pityriasis pilaris, a skin disease not described by dermatologists] (Pityriasis pilaris, maladie de la peau non décrite par les dermatologistes)." (in French). Gazette hebdomadaire de médecine et de chirurgie, Paris 3: 197-201.
- ↑ M. G. A. Devergie and the eponymous named Devergie's disease at Who Named It
- ↑ Pityriasis rubra pilaris. DermNZ (New Zealand Dermatological Society) (26 Dec 2006). Retrieved on 2007-05-08. - describes the various forms
External links
- PRP Support Group - information regarding day-to-day care and medical treatment and having an international membership.
- skin diseases Information
- Dr. Griffith (June 1998). in Editors Champion R.H., Burton J.L., Burns D.A. and Breathnach S.M.: Textbook of Dermatology, 6th edition, 1539–1545. ISBN 0632050640.
Acknowledgement and Attribution Regarding Sources of Content
Some of the initial content on this page may be incorporated in part from copyleft sources in the public domain including wikis such as Wikipedia and AskDrWiki. Drug information for patients came from the The National Library of Medicine. Infectious disease information may have come from the Centers for Disease Control (CDC). Differential Diagnoses are drawn from clinicians as well as an amalgamation of 3 sources: 1.The Disease Database; 2. Kahan, Scott, Smith, Ellen G. In A Page: Signs and Symptoms. Malden, Massachusetts: Blackwell Publishing, 2004:3; 3. Sailer, Christian, Wasner, Susanne. Differential Diagnosis Pocket. Hermosa Beach, CA: Borm Bruckmeir Publishing LLC, 2002:7 .
