Superior canal dehiscence

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Superior canal dehiscence
Classification and external resources
ICD-9 386.43

Superior canal dehiscence (SSCD) is a very rare medical condition, first described in 1998 by Lloyd Minor of Johns Hopkins University, causing hypersensitivity to sound in those affected. It is caused by a thinning or absence of the temporal bone overlying the superior semicircular canal of the inner ear. This is thought to result from physical trauma to the skull although there is also some evidence that the defect or susceptibility is congenital. It can be detected by computed tomographic scanning of the affected area of the skull, currently the only reliable way to distinguish SSCD from Meniere's disease Once diagnosed, the break can be repaired by surgical resurfacing of the affected bone or plugging of the superior semicircular canal.

Symptoms

Superior canal dehiscence can affect both hearing and balance, to different extents in different patients.

  • autophony: person's own speech or other self-generated noises (e.g. heartbeat, eye movements) are heard louder than normal
  • dizziness/vertigo: often aggravated by loud noises
  • Tullio phenomenon - nystagmus caused by sounds of a certain pitch and/or volume in the affected ear and/or pressure changes
  • Pulse-synchronous oscillopsia
  • Low-frequency conductive hearing loss
  • In some cases SSCD cause a chronic loss of equilibrium.
  • A feeling of fullness in the affected ear
  • Tinnitus


External links


Acknowledgement and Attribution Regarding Sources of Content

Some of the initial content on this page may be incorporated in part from copyleft sources in the public domain including wikis such as Wikipedia and AskDrWiki. Drug information for patients came from the The National Library of Medicine. Infectious disease information may have come from the Centers for Disease Control (CDC). Differential Diagnoses are drawn from clinicians as well as an amalgamation of 3 sources: 1.The Disease Database; 2. Kahan, Scott, Smith, Ellen G. In A Page: Signs and Symptoms. Malden, Massachusetts: Blackwell Publishing, 2004:3; 3. Sailer, Christian, Wasner, Susanne. Differential Diagnosis Pocket. Hermosa Beach, CA: Borm Bruckmeir Publishing LLC, 2002:7 .

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